Diseases considered for pediatric lung transplant include:

Chronic Obstructive Lung Diseases

  • Cystic Fibrosis
  • Bronchiolitis Obliterans
  • Bronchiectasis
  • Bronchopulmonary dysplasia

Restrictive Lung Diseases

  • Surfactant Protein Disorders including Surfactant Protein B and C deficiency, ABCA3 and NKX2.1 (TTF-1) mutations
  • Interstitial lung disease
  • Pulmonary fibrosis (radiation, toxins, medications)
  • Pulmonary alveolar proteinosis

Pulmonary Vascular Diseases

  • Primary pulmonary hypertension
  • Pulmonary hypertension associated with congenital heart disease, repaired or unrepaired
  • Pulmonary atresia with nonconfluent hypoplastic pulmonary arteries
  • Pulmonary venous stenosis
  • Alveolar capillary dysplasia